SOCIETY FOR THE STUDY
OF INBORN ERRORS OF METABOLISM

Previous Garrod Awardees

2024

Dr Mattias Lissing
Stockholm, Sweden

Risk for incident comorbidities, nonhepatic cancer and mortality in acute hepatic porphyria: A matched cohort study in 1244 individuals

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J of Inher Metab Disea - 2023; 46/2: 286–299

2023

Dr Jun Kido
Kumamoto, Japan

Clinical manifestation and long-term outcome of citrin deficiency: Report from a nationwide study in Japan

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J Inherit Metab Dis. 2022;45/3:431–444

2022

PD Dr Med Friederike Hörster
Heidelberg, Germany

Delineating the clinical spectrum of isolatedmethylmalonic acidurias: cblA and mut

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J Inherit Metab Dis. 2021;44:193–214

2021

Prof Laurence Bindoff
Bergen, Norway

Simplifying the clinical classification of polymerase gamma (POLG) disease based on age of onset; studies using a cohort of 155 cases

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J Inherit Metab Dis. 2021; 43(4): 726-736 doi: 10.1002/

 

2020

Dr R Spiegel
Afula, Israel

Clinical, radiological, and genetic characteristics of 16 patients with ACO2 gene defects: Delineation of an emerging neurometabolic syndrome

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J Inherit Metab Dis. 2019; 42(2): 264-275 doi: 10.1002/

Epub 2018 Mar 8; 2018 Jul;41(4):689-698. doi: 10.1007/s10545-018-0157-4

2019

Prof Dr Med Johannes Haberle
Zurich, Switzerland

The impact of ammonia levels and dialysis on outcome in 202 patients with neonatal onset urea cycle disorders

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Epub 2018 Mar 8; 2018 Jul;41(4):689-698. doi: 10.1007/s10545-018-0157-4

2018

Ass Prof Melanie Gillingham
Portland, USA

Triheptanoin versus trioctanoin for long-chain fatty acid oxidation disorders: a double blinded randomized controlled trial

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J Inherit Metab Dis. 2017; 40:831–843

2017

Dr Terry Derks
Groningen, The Netherlands

Glycogen storage disease type III: diagnosis, genotype, management, clinical course and outcome.

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J Inherit Metab Dis. 2016; 39:697-704

2016

Prof Shamima Rahman
London, United Kingdom

Paediatric single mitochondrial DNA deletion disorders: an overlapping spectrum of disease.

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J Inherit Metab Dis. 2015; 38:445-457

2015

Dr Yannis Trakadis
Montreal, Canada

Update on transcobalamin deficiency: clinical presentation, treatment and outcome

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J Inherit Metab Dis. 2014; 37:461-473

2014

Dr F Sedel
Paris, France

Krabbe disease in adults: phenotypic and genotypic update from a series of 11 cases and a review.

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J Inherit Metab Dis. 2013;36:859-68

2013

Dr SE Waisbren
Boston, USA

The adult galactosemic phenotype.



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J Inherit Metab Dis. 2012;35:279-86

2012

Dr M del Socorro Perez Poyato
Barcelona, Spain

Juvenile neuronal ceroid lipofuscinosis: clinical course and genetic studies in Spanish patients.


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J Inherit Metab Dis. 2011;34:1083-93

2011

Prof Dr F A Wijburg
Amsterdam, The Netherlands

Mucopolysaccharidosis type IIIB may predominantly present with an attenuated clinical phenotype.

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J Inherit Metab Dis. 2010;33:759–67

2010

Dr Friederike Hörster
Heidelberg, Germany

Prediction of outcome in isolated methylmalonic acidurias: combined use of clinical and biochemical parameters


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2009

Prof Dr Ute Spiekerkoetter
Dusseldorf, Germany

Management and outcome in 75 individuals with long-chain fatty acid oxidation defects:results from a workshop

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Society for the Study of Inborn
Errors of Metabolism (SSIEM)
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